Search on: BLOOD COAGULATION FACTOR XIII 
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Descriptor English:   Factor XIII 
Descriptor Spanish:   Factor XIII 
Descriptor Portuguese:   Fator XIII 
Synonyms English:   Blood Coagulation Factor XIII
Factor XIII A-Chain
Laki Lorand Factor
Factor XIII A Chain
Factor XIII, Coagulation
Stabilizing Factor, Fibrin
Transamidase, Factor XIII
XIII, Coagulation Factor
Coagulation Factor XIII
Factor XIII Transamidase
Fibrin Stabilizing Factor
Fibrinase
Laki-Lorand Factor  
Tree Number:   D12.776.124.125.475
D23.119.475
Definition English:   A fibrin-stabilizing plasma enzyme (TRANSGLUTAMINASES) that is activated by THROMBIN and CALCIUM to form FACTOR XIIIA. It is important for stabilizing the formation of the fibrin polymer (clot) which culminates the coagulation cascade. 
Indexing Annotation English:   activated form use FACTOR XIIIA
Entry Combination - descr/qualif English:   Factor XIII/deficiency use Factor XIII Deficiency
 
See Related English:   Coagulants
 
History Note English:   1970(1964); for FACTOR XIII TRANSAMIDASE see TRANSGLUTAMINASES (1990-2001) 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AA analogs & derivatives
AN analysis AI antagonists & inhibitors
BI biosynthesis CF cerebrospinal fluid
CS chemical synthesis CH chemistry
CL classification CT contraindications
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   22176 
Unique Identifier:   D005176 

Occurrence in VHL:
 

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